Myocardial fibrosis in desmin-related hypertrophic cardiomyopathy
نویسندگان
چکیده
منابع مشابه
Myocardial fibrosis in desmin-related hypertrophic cardiomyopathy
Desmin-related myopathy (DRM) is known to cause different types of cardiomyopathy. Late gadolinium enhancement cardiovascular magnetic resonance (CMR) has been shown to identify fibrosis in ischemic and non-ischemic cardiomyopathies. We present a rare case of desmin-related hypertrophic cardiomyopathy, CMR revealed fibrosis in the lateral wall of the left ventricle. CMR is superior to conventio...
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Introduction: Accurate delineation of myocardial fibrosis in Late Gadolinium Enhancement on Cardiac Magnetic Resonance (LGE-CMR) has a crucial role in the assessment and risk stratification of HCM patients. As this is time-consuming and requires expertise, automation can be essential in accelerating this process. This study aims to use Unet-based deep learning methods to automate the mentioned ...
متن کامل[Myocardial fibrosis in hypertrophic cardiomyopathy].
Rev Esp Cardiol. 2005;58(5):585-6 585 A 20-year-old man was referred to our myocardial disease unit for family screening. His father presented obstructive hypertrophic cardiomyopathy and had an automatic defibrillator implanted for sustained ventricular tachycardia. His brother had died of sudden death at the age of 12. The patient only reported dyspnea on exertion. In the electrocardiogram (EC...
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Background Fibrosis is a common end-point in pathological processes. It is unclear, however, if diffuse fibrosis occurs early in the pathogenesis of hypertrophic cardiomyopathy (HCM). The purpose of this study was to evaluate the presence of diffuse myocardial fibrosis in children and adolescents with HCM using quantification of T1 changes late after gadolinium administration and to assess for ...
متن کاملDesmin-related restrictive cardiomyopathy.
Restrictive cardiomyopathies may have different etiologies, among which we can point out storage diseases by accumulation of different materials such as desmin. Desminopathies are uncommon diseases that progress with conduction abnormalities, peripheral myopathies, and ventricular dysfunction. The present report describes a patient with complete atrioventricular block as the initial event; he l...
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ژورنال
عنوان ژورنال: Journal of Cardiovascular Magnetic Resonance
سال: 2010
ISSN: 1532-429X
DOI: 10.1186/1532-429x-12-68